EN
TÜRKÇE
Poster - 59
Children and young people with oesophageal atresia and/or tracheoesophageal fistula have a high burden of care and significant respiratory complications: a 20 year experience in a tertiary paediatric centre
K Rose*, L Brown*, P Lawrence*, F Murphy**, J Minford**, R Partridge**, A Donne***, J Ducey**, R Thursfield*
*Department of Paediatric Respiratory Medicine Alder Hey Children’s Hospital NHS Foundation Trust Liverpool, United Kingdom
**Department of Paediatric Surgery Alder Hey Children's Hospital NHS Foundation Trust Liverpool, United Kingdom
***Department of Otolaryngology Alder Hey Children's Hospital NHS Foundation Trust Liverpool, United Kingdom
Purpose: Oesophageal atresia (OA) and tracheoesophageal fistula (TOF) are congenital malformations that can affect lung development and subsequently respiratory health.
The aim of this study was to define the burden of care and respiratory complications as experienced by children and young people with oesophageal atresia and/or tracheoesophageal fistula (OA/TOF) seen in our regional paediatric centre.
Method: Search criteria for all patients with a diagnosis of OA/TOF attending the hospital over the past 20 years was used to identify patients. Electronic health records, including medical notes, clinic letters, lung function data and radiology reports were identified and used to gain retrospective data.
Results: We identified a total of 219 patients with a diagnosis of oesophageal atresia/tracheoesophageal fistula.
50% of patients had other congenital structural abnormalities and required input from multiple clinical teams.
Oesophageal dilatations were frequently required in our patient group. Patients required between 0 and 24 dilatations throughout their childhood, with a median of 3, and 8% of patients required 10 or more.
Approximately 50% patients are seen in our joint respiratory / surgical TOF MDT for respiratory symptoms. 23% of patients had required hospitalisation for lower respiratory tract infection.
Tracheobronchomalacia requiring surgical treatment was seen in 9 patients with 6 (2.7%) requiring aortopexy, and 4 (1.8%) requiring tracheostomy.
60 patients (27%) had documented spirometry results with 17 (8%) having reduced lung function (FEV1 <75% predicted) and 4 (1.8%) having severely reduced lung function (FEV1 <50% predicted). The most common pattern found in those with abnormal spirometry results was a restrictive pattern.
Conclusions: We present a 20 year experience of OA/TOF and its associated burden of care and respiratory complications in these patients. Respiratory symptoms are common in these children and a small but significant number have reduced lung function.
K Rose*, L Brown*, P Lawrence*, F Murphy**, J Minford**, R Partridge**, A Donne***, J Ducey**, R Thursfield*
*Department of Paediatric Respiratory Medicine Alder Hey Children’s Hospital NHS Foundation Trust Liverpool, United Kingdom
**Department of Paediatric Surgery Alder Hey Children's Hospital NHS Foundation Trust Liverpool, United Kingdom
***Department of Otolaryngology Alder Hey Children's Hospital NHS Foundation Trust Liverpool, United Kingdom
Purpose: Oesophageal atresia (OA) and tracheoesophageal fistula (TOF) are congenital malformations that can affect lung development and subsequently respiratory health.
The aim of this study was to define the burden of care and respiratory complications as experienced by children and young people with oesophageal atresia and/or tracheoesophageal fistula (OA/TOF) seen in our regional paediatric centre.
Method: Search criteria for all patients with a diagnosis of OA/TOF attending the hospital over the past 20 years was used to identify patients. Electronic health records, including medical notes, clinic letters, lung function data and radiology reports were identified and used to gain retrospective data.
Results: We identified a total of 219 patients with a diagnosis of oesophageal atresia/tracheoesophageal fistula.
50% of patients had other congenital structural abnormalities and required input from multiple clinical teams.
Oesophageal dilatations were frequently required in our patient group. Patients required between 0 and 24 dilatations throughout their childhood, with a median of 3, and 8% of patients required 10 or more.
Approximately 50% patients are seen in our joint respiratory / surgical TOF MDT for respiratory symptoms. 23% of patients had required hospitalisation for lower respiratory tract infection.
Tracheobronchomalacia requiring surgical treatment was seen in 9 patients with 6 (2.7%) requiring aortopexy, and 4 (1.8%) requiring tracheostomy.
60 patients (27%) had documented spirometry results with 17 (8%) having reduced lung function (FEV1 <75% predicted) and 4 (1.8%) having severely reduced lung function (FEV1 <50% predicted). The most common pattern found in those with abnormal spirometry results was a restrictive pattern.
Conclusions: We present a 20 year experience of OA/TOF and its associated burden of care and respiratory complications in these patients. Respiratory symptoms are common in these children and a small but significant number have reduced lung function.